A form of long QT syndrome that is associated with congenital deafness. It is characterized by abnormal cardioelectrophysiology involving the VOLTAGE-GATED POTASSIUM CHANNEL. It results from mutation of KCNQ1 gene (Subtype 1 or JLN1) or the KCNE1 gene (Subtype 2 or JLN2).

Synonyms: Surdo Cardiac Syndrome Jervell And Lange-Nielsen Syndrome 1 Jervell-Lange Nielsen Syndrome Jervell and Lange Nielsen Syndrome Jervell And Lange Nielsen Syndrome 1 Syndrome, Cardio-Auditory-Syncope Prolonged QT Interval in EKG and Sudden Death Cardio Auditory Syncope Syndrome Surdo-Cardiac Syndrome Cardio-Auditory-Syncope Syndrome Deafness, Congenital, and Functional Heart Disease Cardioauditory Syndrome of Jervell and Lange Nielsen Jervell and Lange-Nielsen Syndrome Syndrome, Surdo-Cardiac Syndrome, Jervell-Lange Nielsen Jervell Lange Nielsen Syndrome Cardioauditory Syndrome of Jervell and Lange-Nielsen Syndromes, Cardio-Auditory-Syncope Cardio-Auditory-Syncope Syndromes Surdo-Cardiac Syndromes