An hereditary hemolytic uremic syndrome associated with variations in the gene that encodes COMPLEMENT FACTOR H, or the related proteins CFHR1 and CFHR3. Disease often progresses to CHRONIC KIDNEY FAILURE without the prodromal symptoms of ENTEROCOLITIS and DIARRHEA that characterize typical hemolytic uremic syndrome.

Synonyms: Non Shiga Like Toxin Associated HUS, HUS, Non-Shiga-Like Toxin-Associated, HUS, Nonenteropathic, Hemolytic Uremic Syndrome, Atypical, Toxin-Associated HUSs, Non-Shiga-Like, Atypical Hemolytic-Uremic Syndromes, Toxin-Associated HUS, Non-Shiga-Like, HUSs, Non-Shiga-Like Toxin-Associated, Syndromes, Atypical Hemolytic-Uremic, Nonenteropathic HUS, HUSs, Nonenteropathic, Non-Shiga-Like Toxin-Associated HUS, Hemolytic-Uremic Syndromes, Atypical, Atypical Hemolytic-Uremic Syndrome, Nonenteropathic HUSs, Non-Shiga-Like Toxin-Associated HUSs, Hemolytic-Uremic Syndrome, Atypical, Syndrome, Atypical Hemolytic-Uremic, Non-Stx-Hus, Atypical Hemolytic Uremic Syndrome, Non Stx Hus