A disorder characterized by multiple, wide spread cutaneous cysts that often become inflamed and rupture. It is caused by the same mutations in the gene coding for KRT-17 that are causative mutations for Pachyonychia congenita, Type 2. Natal teeth involvement is sometimes associated with steatocystoma multiplex.
Synonyms: Steatocystomas, Multiplex, Multiplex Steatocystoma, Steatocystoma Multiplices, Sebaceous Cysts, Multiple, Sebaceous Cyst, Multiple, Multiple Sebaceous Cysts, Multiple Sebaceous Cyst, Steatocystoma Multiplex, Cyst, Multiple Sebaceous, Multiplex Steatocystomas, Cysts, Multiple Sebaceous, Steatocystoma, Multiplex
Instance information
comment
2013
identifier
D062685