An NAD+ dependent enzyme that catalyzes the oxidation 3-methyl-2-oxobutanoate to 2-methylpropanoyl-CoA. It plays a role in the degradation of VALINE; LEUCINE; and ISOLEUCINE.
Synonyms: alpha Ketoisovalerate Dehydrogenase, 2-Oxoisovalerate Dehydrogenase, Dehydrogenase, alpha-Ketoisovalerate, 2 Oxoisovalerate Dehydrogenase, Dehydrogenase, 2-Oxoisovalerate, 2-Oxoisovalerate Dehydrogenase (Acylating), alpha-Ketoisovalerate Dehydrogenase, EC 1.2.1.25
Instance information
2006; 2-OXOISOVALERATE DEHYDROGENASE (ACYLATING) was indexed under KETONE OXIDOREDUCTASES 1983-2005, under AMINO ACIDS, BRANCHED-CHAIN 1979-1982, under KETO ACIDS 1973-1982, & VALERATES 1973-1979 ,2006(1980); use AMINO ACIDS, BRANCHED-CHAIN 1979, & KETO ACIDS & VALERATES 1973-1979
D050645