A syndrome of multiple defects characterized primarily by umbilical hernia (HERNIA, UMBILICAL); MACROGLOSSIA; and GIGANTISM; and secondarily by visceromegaly; HYPOGLYCEMIA; and ear abnormalities.
Synonyms: Syndrome, Wiedemann-Beckwith (WBS), EMG Syndrome, Syndrome, EMG, Wiedemann-Beckwith Syndrome (WBS), EMG Syndromes, Exomphalos-Macroglossia-Gigantism Syndrome, Syndrome, Wiedemann-Beckwith, Beckwith Wiedemann Syndrome, Wiedemann Beckwith Syndrome, Exomphalos Macroglossia Gigantism Syndrome, Wiedemann-Beckwith Syndromes (WBS), Wiedemann Syndrome, Wiedemann-Beckwith Syndrome, Beckwith-Wiedemann Syndrome, Syndrome, Exomphalos-Macroglossia-Gigantism, Syndrome, Wiedemann, Wiedemann Beckwith Syndrome (WBS), Wiedemann Syndromes, Syndrome, Beckwith-Wiedemann, Exomphalos-Macroglossia-Gigantism Syndromes
Instance information
1983
D001506