An enzyme of the urea cycle which splits argininosuccinate to fumarate plus arginine. Its absence leads to the metabolic disease ARGININOSUCCINIC ACIDURIA in man. EC 4.3.2.1.
Synonyms: Argininosuccinase, N-(L-Argininosuccinate) arginine-lyase, Argininosuccinate Lyase, Lyase, Argininosuccinate, EC 4.3.2.1
Instance information
comment
1991; see LYASES 1975-1990 ,1991(1975); use LYASES 1975-1990
identifier
D001123
Instance relations
Types