A group of idiopathic multifocal posterior uveitis syndromes involving the CHOROID; RETINAL PIGMENT EPITHELIUM; and RETINA. They are characterized by multiple lesions of hypoautofluorescent dots in the FUNDUS OCULI and reduced VISUAL ACUITY. Several entities including BIRDSHOT CHORIORETINOPATHY are HLA-A ANTIGENS serotype A29 positive.
Synonyms: Serpiginous Choroiditides, Diffuse Subretinal Fibrosis Uveitis, Acute Macular Neuroretinopathy, Acute Idiopathic Blind Spot Enlargement Syndrome, Choroidopathy, Punctate Inner, Serpiginous Choroiditis, Choroidopathy, Serpiginous, Acute Macular Neuroretinopathies, Macular Neuroretinopathy, Acute, Serpiginous Choroidopathy, Punctate Inner Choroidopathy, APMPPE, Acute Posterior Multifocal Placoid Pigment Epitheliopathy, Punctate Inner Choroidopathies, MEWDS, Multiple Evanescent White Dot Syndrome, Choroiditis, Serpiginous, Serpiginous Choroidopathies, Inner Choroidopathy, Punctate, White Dot Syndrome, White Dot Syndromes, Neuroretinopathy, Acute Macular
Instance information
2020
D000080363