|
Increased iduronate sulfatase level
|
HP_0003538 |
[An increased level of iduronate-2-sulfatase activity in the blood.] |
|
Subsarcolemmal accumulations of abnormally shaped mitochondria
|
HP_0003548 |
[An abnormally increased number of mitochondria in the cytoplasma adjacent to the sarcolemma (muscle cell membrane), whereby the mitochondria also possess an abnormal morphology.] |
|
Shoulder girdle muscle weakness
|
HP_0003547 |
[The shoulder, or pectoral, girdle is composed of the clavicles and the scapulae. Shoulder-girdle weakness refers to lack of strength of the muscles attaching to these bones, that is, lack of strength of the muscles around the shoulders.] |
|
Increased circulating pyruvate concentration
|
HP_0003542 |
[The concentration of pyruvate in the blood circulation is above the upper limit of normal.] |
|
Increased level of propylene glycol in blood
|
HP_0410069 |
[An increase in the level of propylene glycol in the blood.] |
|
L-asparaginate
|
CHEBI_32650 |
[An optically active form of asparaginate having L-configuration.] |
|
asparaginate
|
CHEBI_32660 |
[An alpha-amino-acid anion that is the conjugate base of asparagine, arising from deprotonation of the carboxy group.] |
|
Urinary glycosaminoglycan excretion
|
HP_0003541 |
[Excretion of glycosaminoglycan in the urine. Glycosaminoglycans are long unbranched polysaccharides consisting of a repeating disaccharide unit.] |
|
obsolete Increased level of L-glutamic acid in blood
|
HP_0410068 |
|
|
L-asparaginium
|
CHEBI_32651 |
|
|
asparaginium
|
CHEBI_32661 |
|
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Increased level of hippuric acid in blood
|
HP_0410065 |
[An increase in the level of hippuric acid in the blood.] |
|
Increased level of galactitol in red blood cells
|
HP_0410064 |
[An increase in the level of galactitol in the red blood cells.] |
|
Increased level of L-fucose in urine
|
HP_0410067 |
[An increase in the level of L-fucose in the urine.] |
|
primary amine
|
CHEBI_32877 |
[A compound formally derived from ammonia by replacing one hydrogen atom by a hydrocarbyl group.] |
|
Increased level of hippuric acid in urine
|
HP_0410066 |
[An increase in the level of hippuric acid in the urine.] |
|
Increased level of galactitol in plasma
|
HP_0410061 |
[An increase in the level of galactitol in the plasma.] |
|
Decreased level of D-mannose in urine
|
HP_0410060 |
[A decrease in the level of D-mannose in the urine.] |
|
Increased level of galactonate in red blood cells
|
HP_0410063 |
[An increase in the level of galactonate in the red blood cells.] |
|
Increased level of galactitol in urine
|
HP_0410062 |
[An increase in the level of galactitol in the urine.] |